Polyostotic fibrous dysplasia (PFD) is a scarce noncancerous bone condition characterized by the failure to form mature lamellar bone and arrest in the form of woven bone, resulting in deformities and functional limitations. Extreme forms of craniofacial fibrous dysplasia can lead to leontiasis ossea, an exceptionally uncommon presentation. We report a case of a 32-year-old man displaying facial abnormalities indicative of leontiasis ossea. Through radiographic and histopathological assessments, the diagnosis of PFD was confirmed. Surgical intervention was undertaken to address symptoms and enhance facial appearance. This case underscores the diagnostic and therapeutic complexities associated with PFD featuring leontiasis ossea and underscores the significance of a collaborative medical approach.
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Aram et al. (2024) studied this question.
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