Desmoid Tumor in a Patient With Familiar Adenomatosis Polyposisis

Desmoid tumors (TD), also known as aggressive fibromatosis or musculoaponeuritic fibromatosis, are rare, benign, non-metastatic, locally infiltrative neoplasms that originate from soft tissues or muscularaponeurotic structures.Goal: To report a rare case of a patient with desmoid tumor with a history of familial adenomatosis polyposis (PAF).Case report: Male patient, 32 years old, with a family history of FAP, underwent protocolectomy with ileo-rectal reconstruction in 2021.In 2023, the patient noticed the presence of a solid, painless mass on the right flank.Computed tomography of the total abdomen was performed.with contrast, a large heterogeneous mass was revealed, measuring 11.5 x 9.5 x 12.0 cm (W x AP x T), suggestive of Desmoid Tumor.Submitted to tumor resection with rotation of a muscle flap and enterectomy with burial-anastomosis.Discussion/Final Considerations: These tumors often occur in the abdominal wall.Imaging exams assist in diagnosis and can determine the approach modality.Surgical resection with a histologically negative margin has been indicated as an approach for this disease in most cases.