Erdheim-Chester Disease (ECD) is a malignant disease of myeloid progenitor cells that predominantly affects elderly men. ECD is considered a clonal disorder and inflammation corroborates to disease progression and organ injury. Clinical manifestations differ according to the extent and distribution of the involved sites. At diagnosis, most patients exhibit bone involvement, and the majority also present with involvement of at least one extraosseous site. This report describes a 54-year-old man who was diagnosed with ECD following histopathological examination of the sphenoid sinus mucosa.
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Deborah Castro Ferreira de Oliveira (2024) studied this question.
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