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May 7, 2026Asian Journal of Neurosurgery

Erdheim–Chester Disease Mimicking as Multiple Meningioma—A Case Report with Review of Literature

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Authors

KMKrishna Rekha MantryPt. Jawahar Lal Nehru Memorial Medical CollegeLRLavlesh RathorePt. Jawahar Lal Nehru Memorial Medical CollegeGAGarima AgrawalPt. Jawahar Lal Nehru Memorial Medical College

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Overview

Case report reveals a misidentified meningioma in Erdheim–Chester disease, highlighting histiocytosis implications.

Key Points

  • To report a rare case of Erdheim–Chester disease mimicking multiple meningiomas and discuss its clinical implications.
  • Case report of a patient with meningeal mass lesions mistaken for meningiomas
  • Histopathological examination confirmed histiocytosis
  • Multisystemic evaluation and molecular studies were performed
  • Meningeal involvement of Erdheim–Chester disease was confirmed
  • Histopathology identified histiocytosis
  • Patient received systemic treatment with vemurafenib

Cite This Study

Mantry et al. (2026) studied this question.

synapsesocial.com/papers/69fbe382164b5133a91a2c5ahttps://doi.org/10.1055/s-0046-1819609
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Also Consider

Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context:

  1. 1Erdheim-Chester Disease Mimicking a Precentral Meningioma: A Case of Rapid Parenchymal Recurrence and Multisystemic Progression2026
  2. 2Erdheim-Chester Disease Mimicking a Malignant Pituitary Stalk Tumor With Ventricular Dissemination: A Case Report2025
  3. 3Erdheim-Chester disease with predominant cerebellar manifestations: a case report with literature review.2025
  4. 4EP14.04 ERDHEIM-CHESTER DISEASE WITH CENTRAL NERVOUS SYSTEM INVOLVEMENT: A RARE CASE REPORT2025
  5. 5Erdheim‑Chester disease of multisystem involvement with delayed diagnosis: A case report and literature review2024 · 2 citations