Choledochal Cyst Type Three Diagnostic and Management Approach

Choledochal cysts are biliary tree congenital cysts that could be extrahepatic or intrahepatic and have premalignancy potential depending on their type and pathophysiological consequences.Though usually asymptomatic, patients may present with palpable masses or cholestasis-related symptoms.The therapeutic intervention depends on the cyst type.We present a rare case of type three, Todani classification, choledochal cyst in a 26-year-old male patient who presented with acute on top of chronic pancreatitis.The aim is to present rare case therapeutic approaches based on the current literature.Acute obstruction-related cystic dilatation impacts the decision on the best therapeutic approach for such patients, and hepatobiliary surgery experts' elaboration and longer follow-up are needed.Core Tip: Malignant transformation assessment is an essential element in the type three choledochal cyst management plan, as there is no guideline that facilitates the selection of the best therapeutic intervention.