Monostotic fibrous dysplasia of the temporal bone

Fibrous dysplasia is a slow-growing, benign condition characterised by the progressive replacement of normal bone with the abnormal proliferation of fibrous tissue. Over time, this can result in weakened bone and may lead to pain, deformity and fractures. We hereby present a rare case of fibrous dysplasia in a 15 year old female patient who presented with a one-month history of right sided hearing loss together an unusual finding of an ipsilateral aneurysmal temporal bone cyst. In this article, we discuss the clinical features, radiological findings, progression and the surgical management of temporal bone fibrous dysplasia.