Incidental Adult Polysplenia, Interrupted Inferior Vena Cava with Azygos Continuation and Semiannular Pancreas

Polysplenia syndrome is a rare condition (about 2.5:100,000 live births) wherein a person has two or more spleens with accompanying various thoracic and abdominal organ abnormalities. Polysplenia is usually associated with situs ambiguous, while polysplenia with situs inversus is very rare. Herein, we report a rare case of incidentally found polysplenia syndrome in a 40-year-old female who had an interrupted inferior vena cava (IVC) with azygos continuation and also semiannular pancreas, which is a rare finding.