Treatment of scleromyxedema with low doses of intravenous immunoglobulin: report of a case

Scleromyxedema is a rare disease with a chronic course and unknown etiopathogenesis. It is characterized by dermal mucin deposits, fibrosis, and proliferation of fibroblasts in the dermis. Clinically it manifests with an eruption of waxy papules and induration of the skin. It can be accompanied by systemic involvement and be associated with other diseases. Its treatment is not standardized and is currently based on case reports. We present the clinical case of a patient with scleromyxedema who received treatment with intravenous immunoglobulin in doses lower than those recommended in the literature associated with systemic corticotherapy with a good response.