Neuromyelitis Optica Spectrum Disorder (NMOSD) is an autoimmune disorder characterized by central nervous system (CNS) demyelination, autoantibodies against aquaporin-4 (AQP4-Ab), and a higher prevalence in Asian.[1] Diagnosis is often challenged due to varying presentations. We report an atypical NMOSD case featuring an unusual cerebral spinal fluid (CSF) profile mimicking CNS infection.
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Dirks et al. (2024) studied this question.
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