Mounier-Kuhn Syndrome (MKS) is a rare congenital disorder characterized by the abnormal dilatation of the major airways, namely trachea and stem bronchi. It can be presented as the recurrent lower respiratory tract infection. Symptoms may vary from being asymptomatic to a wide range of infections which may lead to severe respiratory failure. Diagnosis can be performed by the means of computed tomography and bronchoscopy. The treatment is primarily symptomatic and supportive. Herein, we have presented a case of a 64-years old man, ex-smoker, who was referred after 4 episodes of antibiotic treated pulmonary infection. He was previously diagnosed with tracheobronchomegaly through CT scan in 2015. We have compared the lung function test and the radiological features between two time slots being 8 years apart (2015-2023), that showed insignificant change.
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Pradeesh Sivapalan (2024) studied this question.
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