Fascinating Image of Pentalogy of Cantrell: Navigating Challenges for Optimal Anesthesia Care

Education| May 2024 Fascinating Image of Pentalogy of Cantrell: Navigating Challenges for Optimal Anesthesia Care Rosa Maria Lopez-Rincon, M.D.; Rosa Maria Lopez-Rincon, M.D. 1Department of Anesthesiology and Perioperative Medicine, Wellstar MCG Health, Augusta, Georgia. Search for other works by this author on: This Site PubMed Google Scholar Miguel Plaza-Lloret, M.D.; Miguel Plaza-Lloret, M.D. 2Department of Anesthesiology and Perioperative Medicine, Wellstar MCG Health, Augusta, Georgia. Search for other works by this author on: This Site PubMed Google Scholar Gustavo Munoz-Monaco, M.D.; Gustavo Munoz-Monaco, M.D. 3Department of Anesthesiology and Perioperative Medicine, Children's Hospital of Georgia, Augusta, Georgia. Search for other works by this author on: This Site PubMed Google Scholar Ana Corina Mavarez, M.D. Ana Corina Mavarez, M.D. 4Department of Anesthesiology and Perioperative Medicine, Children's Hospital of Georgia, Augusta, Georgia. https://orcid.org/0000-0003-4597-440X Search for other works by this author on: This Site PubMed Google Scholar Author and Article Information Published online first on March 1, 2024. Address correspondence to Dr. Lopez-Rincon: Anesthesiology May 2024, Vol. 140, 1016–1017. https://doi.org/10.1097/ALN.0000000000004877 Views Icon Views Article contents Figures & tables Video Audio Supplementary Data Peer Review Share Icon Share Facebook Twitter LinkedIn Email Cite Icon Cite Get Permissions Search Site Citation Rosa Maria Lopez-Rincon, Miguel Plaza-Lloret, Gustavo Munoz-Monaco, Ana Corina Mavarez; Fascinating Image of Pentalogy of Cantrell: Navigating Challenges for Optimal Anesthesia Care. Anesthesiology 2024; 140:1016–1017 doi: https://doi.org/10.1097/ALN.0000000000004877 Download citation file: Ris (Zotero) Reference Manager EasyBib Bookends Mendeley Papers EndNote RefWorks BibTex toolbar search Search Dropdown Menu toolbar search search input Search input auto suggest filter your search All ContentAll PublicationsAnesthesiology Search Advanced Search Topics: anesthesia care, pentalogy of cantrell Pentalogy of Cantrell is a rare congenital condition with an incidence of one case for every 65,000 to 200,000 live births with around 250 probably underreported cases described in modern literature.1 Pentalogy of Cantrell consists of five midline birth defects in their complete form, which include ectopia cordis, supraumbilical abdominal wall defect, sternal cleft, diaphragmatic pericardial defect, and anterior diaphragmatic hernia. It is the result of abnormal development in the ventral mesoderm on the third week after conception with the lateral mesodermal folds failing to migrate to the midline.2 A fetal ultrasonography during the first trimester may be used for the diagnosis, and an echocardiography performed at birth would demonstrate cardiac defects that can be missed if performed intrauterine.3 Figures 1 and 2 show a 2-day-old male, 2.13 kg, born at 33 weeks' gestation via vaginal delivery without prenatal care with Pentalogy of Cantrell diagnosed after... You do not currently have access to this content.