Case report reveals misdiagnosed intracranial masson tumor in a young male, highlighting diagnostic challenges.
The synonymous of intravascular papillary endothelial hyperplasia (IPEH) is masson tumor. IPEH most frequently occurs extracranially in the skin of the face, skull, neck, and trunk and can easily be mistaken clinically, radiologically, and histologically for angiosarcoma, organizing hematoma, or other vascular malformations. Mean age of discovery is between 12 and 70 with a female predominance. Intracranial Masson tumor is a benign lesion that is thought to originate from a reactionary process in response to compromised blood flow Although relatively rare, its accurate diagnosis is very essential since it can clinically be similar, to both benign and malignant lesions. Differential diagnoses of neurological locations of IPEH are more often an angiosarcoma, or meningioma, and metastasis. IPEH are often localized close to the venous sinus or can be developed in a vascular malformation, thrombus, or aneurysm. It is a tricky entity because of its tendency to recur when gross total resection is not achieved. The curative treatment is total resection but recurrence has been reported, long-term follow-up with MRI is recommended. Until December 2022, 47 cases of intracranial IPEH have been reported in peer-reviewed literature. Hereby we present a rare case in young 20-year-old male, which was misdiagnosed radiologically, as well as intraoperatively. Final diagnosis was given histopathological and immunohistochemistry.
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Yadav et al. (2026) studied this question.
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