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April 23, 2016CirculationOpen Access

Nonbiopsy Diagnosis of Cardiac Transthyretin Amyloidosis

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Authors

Julian D. Gillmore
Julian D. GillmoreHeart Failure / Cardiomyopathy
MMMatthew J. MaurerGeneral CardiologyRFRodney H. FalkHeart Failure & Transplant

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Implication

Randomized trial examines noninvasive criteria for diagnosing cardiac ATTR amyloidosis, suggesting improved accuracy without histology.

Key Points

  • The aim is to establish a reliable noninvasive diagnostic method for cardiac ATTR amyloidosis without histology.
  • Utilized bone scintigraphy for diagnosis.
  • Developed noninvasive diagnostic criteria.
  • Focused on patients without monoclonal gammopathy.
  • Diagnosis made reliably without histology.
  • Criteria applicable to the majority of ATTR amyloidosis patients.
  • Improved diagnosis may enhance patient outcomes.

Cite This Study

Gillmore et al. (2016) studied this question.

synapsesocial.com/papers/69aea5047defb997d5abdda4https://doi.org/10.1161/circulationaha.116.021612
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Also Consider

Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context:

  1. 1Pathogenesis of and Therapeutic Strategies to Ameliorate the Transthyretin Amyloidoses2008 · 136 citations
  2. 2Bone scintigraphy with 99m technetium-hydroxymethylene diphosphonate allows early diagnosis of cardiac involvement in patients with transthyretin-derived systemic amyloidosis2014 · 149 citations
  3. 399m Tc-Pyrophosphate Scintigraphy for Differentiating Light-Chain Cardiac Amyloidosis From the Transthyretin-Related Familial and Senile Cardiac Amyloidoses2013 · 625 citations
  4. 4Cardiovascular Magnetic Resonance in Cardiac Amyloidosis2005 · 986 citations
  5. 5Classification of amyloidosis by laser microdissection and mass spectrometry–based proteomic analysis in clinical biopsy specimens2009 · 918 citations