Successful Management of a Solitary Retinal Capillary Hemangioblastoma in a Stepwise Approach

Retinal capillary hemangioblastoma (RCH) is a vascular tumor often associated with Von Hippel–Lindau disease. Solitary RCHs are rare. We report a case of an adolescent boy with sporadic solitary RCH presenting with RCH-associated exudative retinal detachment. Initial treatment with intravitreal triamcinolone reduced subretinal fluid. Subsequent laser ablation of the lesion resulted in a reduction of the lesion size, but traction set in with the opacification and contraction of the hyaloid overlying the lesion. Pars plana vitrectomy with membrane peeling and gas tamponade was performed, leading to retinal attachment and visual improvement. Management of RCH should be individualized based on lesion location and associated retinal changes (exudation or traction).