WCN26-5532 Successful Transition to Peritoneal Dialysis in a Patient with Fontan-Associated End-Stage Kidney Disease

The Fontan procedure has markedly improved the prognosis of patients with single-ventricle physiology. However, long-term survivors often develop multiorgan dysfunction caused by chronic venous congestion, known as Fontan-associated disorders. Renal dysfunction in this population, termed Fontan-associated nephropathy, is thought to result from sustained venous congestion and decreased renal perfusion. The optimal renal replacement therapy (RRT) for these patients has not been established, and hemodialysis (HD) is often limited by hemodynamic instability.