Ebstein-like Anomaly of the Mitral Valve in an Infant: an Unrepairable Entity?

Background: “Ebstein’s anomaly of the mitral valve” or “Ebstein–like anomaly of the mitral valve” is a rare disease entity involving the posterior mitral leaflet. Case Presentation: We report the surgical case of an 11-month-old male with mitral regurgitation and atrial septal defect. Echocardiogram revealed significant tethering and downward displacement of the posterior leaflet, along with a relative prolapse of the anterior leaflet—an anatomy consistent with an “Ebstein’s-like anomaly of the mitral valve.” During the initial operation, artificial chords were placed, but this intervention further widened the gap between the leaflets. As a result, the patient eventually required mitral valve replacement. Conclusions: Ebstein-like anomaly of the mitral valve is a disorder that is difficult to manage with standard repair techniques. In most cases, prosthetic valve replacement may be difficult.