An Oddball Coexistence: Ebstein’s Anomaly with Rheumatic Mitral Valve Disease Surviving into Late Adulthood

Ebstein’s anomaly is an infrequent congenital malformation of the heart , in which the septal and posterior leaflets of the tricuspid valve are displaced to the apex, leading to partial “atrialization” of the right ventricle. Its clinical presentation varies widely, contingent on its severity and any co-occurring cardiac anomalies. Although most cases are identified in childhood, some individuals remain asymptomatic and may not be diagnosed until later in life. Conversely, rheumatic mitral valve disease represents one of the major causes of acquired cardiac disorders among children and young adults, particularly in developing regions such as India. Despite a significant decline in rheumatic heart disease incidence in India recently, it still poses a major public health challenge. Existing rheumatic heart disease studies report an average prevalence of 0.5 per 1,000 children aged 5-15 years. This report details the unusual co-occurrence of Ebstein’s anomaly and mitral valve stenosis rheumatic in origin in a 65-year-old man, a rare finding in an unoperated patient of this age.