Does right ventricular functional reserve during exercise differ between patients with SSc-PAH and IPAH?
RV dilation during exercise can predict adverse ventricular-vascular coupling in PAH patients, with SSc-PAH patients demonstrating worse RV contractile reserve than those with IPAH.
RV contractile reserve is depressed in SSc-PAH versus IPAH subjects, associated with reduced calcium recycling. During exercise, this results in ventricular-pulmonary vascular uncoupling and acute RV dilation. RV dilation during exercise can predict adverse ventricular-vascular coupling in PAH patients.
Hsu et al. (Thu,) studied this question.
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