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July 24, 2023HeartOpen Access

Ebstein’s anomaly in children and adults: multidisciplinary insights into imaging and therapy

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Why the study?

Ebstein's anomaly carries an increased risk of mortality, and appropriate timing of intervention is challenged by a wide disease spectrum and paucity of data on patient-tailored interventional strategies.

Population

Children and adults with post-neonatal Ebstein's anomaly

Design

Review

Authors

GPGiulia PasqualinABAntonio BoccellinoMCMassimo Chessa

Discussion

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Overview

Questions watchful waiting in asymptomatic Ebstein's anomaly; leaves open optimal intervention timing given low-certainty evidence.

Structured PICO

P
Population
Children and adults with post-neonatal manifestations of Ebstein's anomaly

A multidisciplinary approach utilizing multimodality imaging is necessary for proper risk stratification and timely intervention in Ebstein's anomaly, as delayed intervention worsens outcomes.

Cite This Study

Pasqualin et al. (2023) studied this question.

synapsesocial.com/papers/69d570ea75589c71d767e01ehttps://doi.org/10.1136/heartjnl-2023-322420
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Also Consider

Synapse has enriched 4 closely related papers on similar clinical questions. Consider them for comparative context:

  1. 1Contemporary outcomes and mortality risks of Ebstein anomaly: A single‐center experience in Thailand2019 · 9 citations
  2. 2Detection of early signs of right ventricular systolic impairment in unoperated Ebstein’s anomaly by cardiac magnetic resonance feature tracking2022 · 7 citations
  3. 3Haemodynamic determinants of improved aerobic capacity after tricuspid valve surgery in Ebstein anomaly2020 · 35 citations
  4. 4Catheter Ablation of Arrhythmias in Ebstein's Anomaly: A Multicenter Study2011 · 109 citations