Anatomy of the Pulmonary Circulation and Outcomes in Tetralogy of Fallot With Major Systemic‐to‐Pulmonary Collaterals and Unilateral Pulmonary Artery of Ductal Origin

The presence of with a DA supplying all flow to 1 normally arborizing PA, almost always the left PA, and MAPCAs providing all flow to the other lung, is a distinct anatomic subset of TOF/MAPCAs. In our practice, stenting of the DA in the neonatal period is the most appropriate therapy, typically followed by PA reconstruction and repair in early infancy, depending on the anatomy of the MAPCAs to the contralateral lung. Outcomes in these patients are generally excellent.