Survival in Marfan's syndrome has likely improved with current guidelines, but high fatality from aortic root dissection highlights the need for better screening and risk stratification.
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Supports guideline-directed care in Marfan syndrome; leaves open need for better dissection prevention in prospective studies.
Survival in the Marfan's syndrome in the past 14 years seems satisfactory; with application of current guidelines, it has probably even improved. However, because of the high fatality rate in Marfan patients developing aortic root dissection, more extensive screening for Marfan's syndrome and a search for additional risk factors are desirable.
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Groenink et al. (1999) studied this question.
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