Why the study?
Primary biatrial rhabdomyosarcomas are extremely rare with only 3 cases reported, and there is no consensus on how to manage them due to the scarcity of cases.
Primary biatrial rhabdomyosarcoma is an extremely rare cardiac tumor with a poor prognosis that is typically managed with surgical excision and chemoradiotherapy.
Documents preserved postoperative function in rare biatrial rhabdomyosarcoma; leaves open optimal adjunctive strategies given dismal survival.
postoperative day. Postoperative cardiac functional tests revealed an ejection fraction of 60%, consistent with the preoperative value, and no mitral valve dysfunction. Biatrial rhabdomyosarcomas are extremely rare, with only 3 cases reported, including ours, reported in the literature, to the best of our knowledge. Transthoracic echocardiogram is useful in the diagnosis. They require surgical excision along with chemotherapy or radiotherapy. Their prognosis is poor, with a median survival of almost one year. Primary biatrial rhabdomyosarcoma is an extremely rare diagnosis that can present with symptomatology based on the location, size, and number of masses. There is no consensus on how to manage them due to the scarcity of cases, but they are managed as single rhabdomyosarcomas. The majority require surgical excision, with subsequent chemotherapy or radiotherapy. The prognosis is very poor, with the majority of the patients not surviving longer than one year.
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Panagiotopoulos et al. (2023) studied this question.
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