Parachute mitral valve is a rare cause of congenital mitral stenosis that can occasionally remain undiagnosed until adulthood, presenting with severe pulmonary hypertension.
Parachute mitral valve may present in adulthood with severe stenosis and pulmonary hypertension; extends the recognized spectrum of this rare anomaly.
Congenital mitral stenosis involves the annulus, the zone immediately above and contiguous with the annulus, the leaflets, the chordae tendineae, and the papillary muscles. In a parachute mitral valve (PMV), all chordae tendineae which are usually shorter and thicker than normal type, inserted into this single papillary muscle. This condition restricts the motion of leaflets and obstructs the blood flow into the left ventricle during diastole. Here we present two cases of severe congenital mitral stenosis with severe pulmonary hypertension due to parachute mitral valve that allowed survival into adulthood without any specific treatment.
No takes yet. Share an insight, caveat, or question.
Bade et al. (2018) studied this question.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: