Population
9 patients with diffuse pulmonary lymphangiomatosis, mean age at presentation 10 years.
Design
Case_series
Authors
Loading...
May prompt consideration of this rare lesion in progressive pediatric pulmonary lymphatic disease; leaves open need for prospective validation and targeted therapies.
Diffuse pulmonary lymphangiomatosis is a distinct, progressive, and potentially fatal lymphatic vascular lesion of the lung, particularly aggressive in young children.
Tazelaar et al. (1993) studied this question.
Synapse has enriched one closely related paper. Consider it for comparative context: