Key result
A review of available data on Carney complex, a rare hereditary syndrome associated with multiple endocrine neoplasias, heart and skin myxomas, and lentiginosis, is presented.
This paper provides a review of Carney complex, a rare hereditary syndrome that can present with heart myxomas.
May aid recognition of Carney complex in myxoma patients; leaves open need for prospective management studies.
Carney complex is a rare hereditary syndrome characterized by an autosomal-dominant mode of inheritance and associated with multiple neoplasias affecting endocrine organs. The typical manifestations of this syndrome include pigmented micronodular adrenal dysplasia, lentiginosis, heart and skin myxomas, giant cell sertoliomas, and some other neoplasias. To date, a few hundred patients with this pathology have been described worldwide. A review of the available data about Carney complex is presented.
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Orlova et al. (2012) conducted a review in Carney complex. A review of available data on Carney complex, a rare hereditary syndrome associated with multiple endocrine neoplasias, heart and skin myxomas, and lentiginosis, is presented.
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