This case highlights that congenital long QT syndrome can present with a simulated acute coronary event in advanced age and can be effectively managed with pacemaker implantation.
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May support pacing for symptom relief in late-diagnosed congenital LQTS; leaves open broader efficacy and optimal strategies.
This report describes the "benign" clinical course of a congenital long QT syndrome (LQTS) simulated acute coronary event in an 85 year old woman who had a history of recurrent syncope accompanied by numerous severe traumatic events from childhood. Her daughter died suddenly. LQTS was diagnosed on the basis of characteristic ECG findings, including a permanently prolonged QT interval, typical dynamic T-wave changes, and runs of torsades de pointes. A permanent DDDR pacemaker was implanted. Eighteen months after implantation there have been no further complaints of dizziness or syncope.
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Khalameizer et al. (2005) studied this question.
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