Key result
Primary splenic angiosarcoma is an aggressive neoplasm with a 69% metastatic rate and an abysmal prognosis, resulting in 79% mortality at a median follow-up of 6 months.
Observational (n=40)
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May prompt earlier specialist referral and trial enrollment; extends clinicopathologic data on this rare, aggressive entity.
Falk et al. (1993) conducted an observational in Primary splenic angiosarcoma (n=40). Primary splenic angiosarcoma was evaluated on Mortality. Primary splenic angiosarcoma is an aggressive neoplasm with a 69% metastatic rate and an abysmal prognosis, resulting in 79% mortality at a median follow-up of 6 months.
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