A multidisciplinary approach including simulation scenarios is recommended for managing pregnant women with rare cardiac conditions like catecholaminergic polymorphic ventricular tachycardia.
Supports multidisciplinary simulation planning for cesarean in CPVT pregnancy; hypothesis-generating for rare cardiac conditions.
In Brief BACKGROUND: Catecholaminergic polymorphic ventricular tachycardia is a genetic disorder in which ventricular tachycardia occurs in the absence of structural heart disease or a prolonged QT interval. If untreated, there is a high incidence of sudden cardiac death. Management of this cardiac condition during pregnancy merits a multidisciplinary approach. CASE: A nulliparous woman with catecholaminergic polymorphic ventricular tachycardia presented at 15 weeks of gestation. Her care involved a multidisciplinary team including cardiology, maternal–fetal medicine, obstetric nursing, cardiac nursing, and anesthesia. A simulation scenario was designed to prepare for cardiac events during labor. A term intrapartum cesarean delivery was performed for fetal indications. CONCLUSION: A multidisciplinary approach to the antepartum, intrapartum, and postpartum care of women with catecholaminergic polymorphic ventricular tachycardia is critical to a team-based successful pregnancy outcome. Obstetrics simulation scenarios and a multidisciplinary plan are encouraged when caring for pregnant women with rare cardiac conditions such as catecholaminergic polymorphic ventricular tachycardia.
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Romagano et al. (2016) studied this question.
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