Hepatoblastoma

Hepatoblastoma is the most common primary hepatic malignancy of childhood. Patients most commonly present with abdominal distension and an elevated alpha-fetoprotein. Patients should be imaged via MRI using a hepatobiliary contrast agent. The PRE-Treatment EXTent of tumor staging systems is used to assess all pediatric liver tumors. Survival rates have improved over the past several decades. While tumor resection is required for a cure, patients also receive neoadjuvant chemotherapy.