Open Thoracoabdominal Aortic Replacement in a Long-Term Survivor of Early-Onset Marfan Syndrome

INTRODUCTION: Early-onset Marfan syndrome (eoMFS) is a rare and severe connective tissue disorder marked by cardiovascular complications in early life. It carries a poor prognosis, often causing death within the first 2 years of life due to heart failure. However, aggressive medical management and early surgical intervention can result in long-term survival, and these patients may subsequently develop aortic disease in early adulthood. Herein, we present a rare case in which we successfully treated an aortic dissection in a patient with eoMFS.