Pneumonectomy in Scimitar Syndrome: anaesthesia management.

Scimitar syndrome is a rare association of congenital cardiopulmonary anomalies consisting of a partial ano- malous pulmonary venous connection of the right lung (part or the entire right lung) to the inferior vena cava, right lung hypoplasia, dextroposition of the heart, and anomalous systemic arterial supply to the right lung. Surgical treatment includes either ligation of anomalous arteries and the scimitar vein implanted into left atrium or resection of sequestrated or chronically infected lung. Anaesthesia management of patients with Scimitar syn- drome is challenging due to coexisting congenital heart disease. The literature on anaesthesia management of patients with Scimitar syndrome undergoing Pneumo- nectomy is rare and hence authors wish to share their experience of anaesthesia management of a case of Sci- mitar syndrome posted for Right Pneumonectomy in view of infected and non-functioning lung.