Ultrawide-field multimodal imaging of unilateral retinal racemose haemangioma in Wyburn-Mason syndrome

Fig. 1: Ultrawide-field multimodal imaging of unilateral retinal racemose hemangioma. Full size image Ultrawide-field fundus imaging of an 8-year-old girl with no relevant systemic or family history revealed multiple markedly dilated and tortuous retinal vessels in the left eye, with several arteriovenous communications forming a racemose distribution extending from the optic disc through all four quadrants to the retinal periphery ( A ), whereas the right fundus was unremarkable. Fundus autofluorescence clearly delineated the distribution of the dilated and tortuous vessels ( B ). Ultrawide-field optical coherence tomography angiography demonstrated enlarged medusa-like vascular channels without evidence of retinal ischaemia ( C ). Corresponding B-scan optical coherence tomography images showed vascular wall thickening, marked luminal dilatation, and anteroposterior tortuosity, with focal associated retinal schisis ( arrows ) ( D ).