Key result
Cardiac magnetic resonance imaging demonstrated complete absence of the entire pericardium in a patient presenting with chest pain.
Case Report (n=1)
Provides cardiac MRI characteristics of an extremely rare case of complete absence of the entire pericardium.
May prompt MRI consideration for rare congenital pericardial absence in atypical chest pain; leaves open prospective data on risks and management.
Congenital absence of the pericardium is a very rare anomaly which has an incidence of 1 in 14000 cases in autopsy studies. Defects in the pericardium are either partial or complete with complete defects having a much benign course than partial defects. Partial defects are associated with complications like strangulation of a herniated cardiac chamber or coronary artery stenosis from external compression. Absence of the left pericardium is the most frequently encountered type of defect which accounts for 2/3 of the cases. We herein report a case of complete absence of the entire pericardium which is an extremely rare subtype with associated Cardiac magnetic resonance images.
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Nellaiyappan et al. (2016) conducted a case report in Congenital complete absence of pericardium (n=1). Cardiac magnetic resonance imaging was evaluated. Cardiac magnetic resonance imaging demonstrated complete absence of the entire pericardium in a patient presenting with chest pain.
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