Key result
Congenital Long QT syndrome can manifest with potentially fatal torsades de pointes arrhythmia late in life in previously asymptomatic elderly patients.
Case Report (n=1)
Congenital Long QT syndrome can present with life-threatening arrhythmias for the first time in late adulthood, highlighting the need for vigilant assessment in families with sudden death.
Alerts clinicians to consider congenital LQTS in elderly with TdP and sudden-death family history; leaves optimal late-life screening open.
We report a case of torsades de pointes arrhythmia as the first manifestation of congenital Long QT syndrome in a 77-year-old man with family history of sudden unexplained death. This case illustrates the importance of vigilant clinical assessment and genetic counseling in families with sudden death in order to identify properly asymptomatic relatives at risk for cardiac events. It also demonstrates that Long QT syndrome can still manifest with potentially fatal arrhythmias late in life in previously asymptomatic elderly patients.
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Asatryan et al. (2017) conducted a case report in Congenital Long QT syndrome (n=1). Congenital Long QT syndrome was evaluated. Congenital Long QT syndrome can manifest with potentially fatal torsades de pointes arrhythmia late in life in previously asymptomatic elderly patients.
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