Key result
In 6 patients with Maffucci's syndrome, spindle-cell hemangioendotheliomas presented as locally recurrent or persistent multicentric lesions that did not metastasize over an average 20-year follow-up.
Population
6 patients with Maffucci's syndrome in whom all vascular lesions were spindle-cell hemangioendothelioma (SCH)
Design
Case_series
Follow-up
averaging 20 years
Authors
Loading...
SCH may predominate in Maffucci syndrome vascular lesions; extends histologic spectrum but leaves diagnostic criteria and surveillance open.
Case Report (n=6)
In Maffucci's syndrome, vascular lesions previously diagnosed as hemangiomas may be spindle-cell hemangioendotheliomas, which are locally recurrent but do not metastasize.
Fanburg et al. (1995) conducted a case report in Maffucci's syndrome with spindle-cell hemangioendotheliomas (n=6). Spindle-cell hemangioendothelioma (SCH) was evaluated on Clinical characteristics and outcomes of SCH. In 6 patients with Maffucci's syndrome, spindle-cell hemangioendotheliomas presented as locally recurrent or persistent multicentric lesions that did not metastasize over an average 20-year follow-up.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: