Cranial Computed Tomographic Scan Appearance of Sturge-Weber Disease: Unusual Presentation

The CT findings in both the typical and atypical presentations of the Sturge-Weber syndrome are characteristic if not pathognomonic in most cases. The typical gyriform cortical calcification and cortical atrophy are well demonstrated whether associated with a small or enlarged hemicranium. Contrast enhancement was demonstrated in both cases where contrast medium infusion was performed.