Why the study?
Adrenocortical carcinoma is a rare malignancy that has been linked with MEN-1, but ectopic extra-adrenal presentations are extremely rare.
Population
A 66-year-old lady with newly diagnosed diabetes and primary hyperparathyroidism
Design
Case report
Authors
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Ectopic ACC may present with new diabetes and hyperparathyroidism; extends MEN-1 spectrum but leaves open diagnostic implications.
This is the first reported case of extra-adrenal adrenocortical carcinoma in a patient with MEN-1 syndrome, highlighting the need for screening and close follow-up of adrenal lesions in this population.
Green et al. (2024) studied this question.