Key result
Primary pulmonary synovial sarcoma presenting as recurrent pneumothorax resulted in severe disease progression and death despite surgical resection and chemotherapy in 1 patient.
Case Report (n=1)
Primary pulmonary synovial sarcoma can present as recurrent pneumothorax and should be considered in the differential diagnosis to avoid misdiagnosis.
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Recurrent pneumothorax may signal rare pulmonary synovial sarcoma; leaves open optimal management for this aggressive tumor.
Primary pulmonary synovial sarcoma (PPSS) is a relatively rare neoplasm with highly progressive potential. We present an extremely rare case of PPSS presenting as recurrent pneumothorax with bullous lesions. Bullectomy was performed at the local hospital. Unfortunately, the patient was initially misdiagnosed as atypical carcinoid. Although a negative resection margin was obtained during the first surgery and a remedial operation and chemotherapy followed, the patient developed severe disease progression and died soon after. This report demonstrates that PPSS can easily be misdiagnosed and should be seriously considered in the differential diagnosis of pneumothorax.
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Guo et al. (2016) conducted a case report in Primary pulmonary synovial sarcoma (n=1). Bullectomy, remedial operation, and chemotherapy was evaluated on Disease progression and death. Primary pulmonary synovial sarcoma presenting as recurrent pneumothorax resulted in severe disease progression and death despite surgical resection and chemotherapy in 1 patient.
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