Population
Patients with Quebec platelet disorder (QPD)
Design
Review
Authors
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Supports antifibrinolytic use in confirmed cases; leaves open broader PLAU testing in unexplained bleeding.
This review summarizes the pathogenesis, diagnosis, and treatment of Quebec platelet disorder, highlighting its unique gain-of-function defect in fibrinolysis.
Blavignac et al. (2011) studied this question.
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