This case report discusses the anesthetic management of a pregnant patient with single ventricle physiology and Fontan circulation undergoing an emergency cesarean birth.
May warrant specialized anesthetic protocols for Fontan cesarean delivery; leaves open optimal strategies pending larger studies.
The incidence of single ventricle physiology is up to 3% among all congenital heart diseases.1 The term ‘single ventricle’ includes a wide variety of congenital heart diseases, including ventricular connections, common ventricle, etc., which all share a common feature of having a single functional ventricle.1-3 Fontan is a common procedure that is used in patients with single ventricles to separate systemic and pulmonary circulations.4 In the absence of a subpulmonic pumping ventricle, pulmonary circulation is highly preload dependent and hemodynamic decompensation can be rapid in the setting of increased demand for cardiac output.
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Mondal et al. (2026) studied this question.
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