Key result
Elevated stool α-1-antitrypsin confirmed protein-losing enteropathy in a patient with constrictive pericarditis secondary to a mediastinal inflammatory myofibroblastic tumor.
Why the study?
Establishing the diagnosis and determining the underlying etiology of constrictive pericarditis is often challenging.
Case Report (n=1)
Protein-losing enteropathy is a rare but important complication of constrictive pericarditis that can present with hypogammaglobulinemia and lymphocytopenia.
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May warrant mediastinal evaluation in atypical constrictive pericarditis; leaves open etiology-specific management.
Schmitt et al. (2021) conducted a case report in Constrictive pericarditis (n=1). Elevated stool α-1-antitrypsin confirmed protein-losing enteropathy in a patient with constrictive pericarditis secondary to a mediastinal inflammatory myofibroblastic tumor.
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