Population
4 male patients from two families with impaired skeletal muscle relaxation that rapidly worsened during…
Design
Case_series
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Confirms type 2 fiber-specific Ca2+-ATPase deficiency in Brody's disease; leaves open therapeutic implications pending larger studies.
Brody's disease is characterized by a deficiency of Ca2+-ATPase in the sarcoplasmic reticulum of type 2 muscle fibers, explaining the impaired muscle relaxation.
Karpati et al. (1986) studied this question.
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