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May 1, 1989Archives of Pediatrics and Adolescent Medicine

Ebstein's Anomaly and Extracardiac Defects

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Population

4 cases of Ebstein's anomaly associated with extracardiac malformations

Design

Case_series

Authors

JSJoseph R. Siebert

Discussion

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Overview

May prompt targeted craniofacial, CNS, and limb evaluation in Ebstein's anomaly; leaves open diverse non-syndromic etiologies.

Structured PICO

P
Population
4 cases of Ebstein's anomaly associated with extracardiac malformations
O
Outcome
Extracardiac changes, karyotypes, and anatomic patterns

Ebstein's anomaly with extracardiac defects often involves craniofacial, CNS, and limb abnormalities without a distinctive syndrome, suggesting diverse etiologies.

Cite This Study

Joseph R. Siebert (1989) studied this question.

synapsesocial.com/papers/6a733db7d98d9ee37dc8f809https://doi.org/10.1001/archpedi.1989.02150170068024
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Also Consider

Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context:

  1. 1Ebstein's Anomaly:1993 · 51 citations
  2. 2Neonatal Ebsteins Anomaly presenting with unique features: Rare case report2024
  3. 3Ebstein anomaly: Report of a familial occurrence and prenatal diagnosis1992 · 31 citations
  4. 4A Rare Tricuspid Anomaly2005
  5. 5Ebstein's Anomaly Associated with Cardiomyopathy and Pulmonary Hypertension1964 · 4 citations