Supraclavicular Island Fascial Flap in the Treatment of Progressive Hemifacial Atrophy

Progressive hemifacial atrophy is a rare disorder, almost 0.30 percent of the , characterized by progressive atrophy some or all tissues on one side of the face, extending to other parts of the body. described by Parry in 1825, the disorder is known as Romberg’s syndrome or Parry- syndrome.1 The disease is unilateral in 95 percent of cases and can be located on both of the body. process may be bilateral in 5 to 10 percent cases. Tissues involved include skin, tongue, , soft palate, cartilage of the nose, ear, subcutaneous , larynx, muscle, and bone. Either may be affected. is believed to be related to scleroderma,2 is not congenital and the cause is not known.3 Onset occurs most often before or during adolescence but occasionally in middle or later years.1 Several reconstructive using autologous4–7 or synthetic 8 have been proposed to restore the symmetry the face, the treatment of choice to date surgery. -tissue reconstruction is mostly performed free, muscle, or fasciocutaneous flaps.9 We a case of a young, diabetic patient with a body habitus affected by Parry-Romberg syndrome which the deepithelialized supraclavicular fascial flap was used to obtain a symmetric of the involved side. flap based on the supraclavicular artery is not as a pure island flap but with a fascial , thin and resistant, which ensures a good . Also, when a higher tension rate is , it avoids risk of excessive traction or kinking the vessels.10 Features and results of the used are reported in the article.