Late Diagnosic of Bicuspid Aortic Valve with Severe Aortic Stenosis and Large Thoracic Aortic Aneurysm: Case Report and Review of the Literature.

Bicuspid aortic valve (BAV) is the most common congenital aortic valve anomaly and affects approximately 1%–2% of the population. Individuals with BAVs have higher risks of valvular dysfunction, endocarditis, and ascending aortic aneurysm and dissection than individuals with tricuspid aortic valves. We report a fatal outcome of ascending aortic aneurysm in a women patient with bicuspid aortic valve complited to aortic sténosis. The patient was qualified for elective surgery of replacement of the affected aorta with composite aortic valve-supracommissural ascending aorta. Unfortunately, patient ended up fatally during the open heart surgery. Congenital BAV are common and in most cases remain undetected, BAVs may progress and become calcied, thus leading to varying degrees of severity of aortic stenosis. The thoracic aortic aneurysm in BAV frequently involves the proximal aorta, including the aortic root, ascending aorta, and aortic arch. While the ascending aortic aneurysm might be affected by both aortopathy and hemodynamics. Our patient, regrettably, was not diagnosed on time with BAV, thus preventive measures were not applied on him can avoid its serious consequences.