Erdheim Chester disease: A case with cutaneous involvement

Erdheim-Chester disease (ECD) is a rare multisystem disease characterized by the proliferation of non-Langerhans histiocytes.It is characterized by excessive production and accumulation of histiocytes in multiple tissues and organs.Sites of involvement may include long bones, skin, eyes, lungs, brain, pituitary gland, and additional tissues and organs.The disease course varies depending on the organ and degree of involvement.In this case report, we presented the case of a 54-year-old female patient diagnosed with ECD, manifesting with squamous, enduring plaque lesions on the skin.