Primary retroperitoneal Ewing's sarcoma in a young woman: A casereport

Ewing's sarcoma (EWS) is a rare malignant tumour that is more likely to occur in children and young people, especially in people of European ancestry, with an annual incidence rate of one in a million, and the incidence of extra-skeletal EWS is even lower, among which retroperitoneal EWS is advanced once detected because of the deep location of the lesion and other characteristics, which makes treatment difficult.The following case report describes an EWS in the retroperitoneal region in a young healthy female patient.A 28-year-old young female patient with a negative family history underwent gynaecologic ultrasound examination for difficulty in defaecation and lower abdominal pain, which revealed a solid cystic mass behind the cervix, tenderness of the mass, and compression of the vagina and rectum.Therefore, surgery was recommended.A retroperitoneal tumour was found during intraoperative exploration, and laparoscopic surgery was changed to open surgery.Postoperative pathology suggested EWS.After postoperative radiation therapy and close follow-up, tumour recurrence occurred six months after surgery, and bone metastasis occurred one year after surgery.Retroperitoneal EWS is a rare and poorly documented disease.Radical surgery remains the first-line treatment of this disease.