Key result
Neoadjuvant chemotherapy followed by surgical resection, including a left nephrectomy, achieved local control of a rare retroperitoneal Ewing sarcoma in a 15-year-old girl.
Why the study?
Ewing sarcoma rarely presents in the retroperitoneum, and multidisciplinary management of these rare presentations needs reporting.
Case Report (n=1)
Retroperitoneal Ewing sarcoma is a rare presentation that may require en bloc resection of adjacent organs, such as the kidney, to achieve adequate local control.
Rare retroperitoneal Ewing sarcoma adherent to kidney reported in adolescent; leaves open optimal surgical and oncologic strategies.
Ewing sarcoma is a small round blue cell tumor that most commonly involves bony structures in the pediatric population. Less commonly, it presents in the soft tissues of other anatomic areas including the limbs and trunk, and rarely, the retroperitoneum. In this report, we present the case of a 15-year-old girl who presented with vague abdominal complaints and was found to have a left retroperitoneal Ewing sarcoma that was densely adherent to, but not arising from the left kidney, as well as a calcified lesion of the left adnexa. She was treated with neoadjuvant chemotherapy and underwent resection via a combined laparoscopic approach for the adnexal mass, and laparotomy for the retroperitoneal Ewing sarcoma, which also required left nephrectomy for adequate local control of the tumor. Given the rarity of this tumor in the retroperitoneal location, this patient's treatment course benefited from a multidisciplinary discussion and plan.
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Qumsiyeh et al. (2021) conducted a case report in Retroperitoneal Ewing sarcoma (n=1). Neoadjuvant chemotherapy and surgical resection (including left nephrectomy) was evaluated on Local control of the tumor. Neoadjuvant chemotherapy followed by surgical resection, including a left nephrectomy, achieved local control of a rare retroperitoneal Ewing sarcoma in a 15-year-old girl.
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