Answers are grounded in this paper and cite their sources.
Most gliomas in neurofibromatosis type 1 (NF1) are pilocytic astrocytomas (PAs) of the optic pathway occurring in young children. However, some individuals develop gliomas that lack the typical NF1-associated clinical features or radiographic appearance. We identified 17 atypical presentations from a review of 100 patients with NF1-associated gliomas. Biopsy showed that 9 were not classic PAs. These data highlight the value of biopsy in NF1-associated gliomas with unusual clinical or radiographic presentations.
No takes yet. Share an insight, caveat, or question.
Perry et al. (2006) studied this question.
Synapse has enriched 10 related papers. Consider them for comparative context: