Patients with Leopard syndrome require thorough and repeated cardiac assessments due to the high prevalence and progressive nature of associated cardiac abnormalities.
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Emphasizes repeated cardiac assessments before anesthesia in Leopard syndrome; leaves open standardized protocols for this rare condition.
'Leopard' syndrome is a rare inherited disorder associated with a high prevalence of cardiac abnormalities. General anaesthesia for dental treatment in a patient who had cardiomyopathy and bizarre electrocardiographic abnormalities associated with this syndrome is described. A thorough cardiac assessment is advised in a patient with multiple lentigines, although no clinical symptoms or signs may be found. Even if no cardiac abnormality is found before it is better to re-assess the patient, since abnormalities may develop later. The assessment should be repeated if any abnormality was detected before but without clinical significance, since the disease is progressive and may progress more rapidly in some patients than in others.
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Rodrigo et al. (1990) studied this question.
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